Mouse models of HD:
• Bates’ R6 transgenic (R6/2)
– Mangiarini et al. (1995) Cell
• cDNA transgenic
– Reddy et al. (1998) Nat Genet 20, 198-202
• N171 transgenic
– Schilling et al. (1999) Hum Mol Genet 8, 397-407
• YAC transgenic
– Hodgson et al. (1999) Cell 23, 181-92
• (CAG)n knock-in
– Wheeler et al. (1999) Hum Mol Genet 8, 115-22
– Shelbourne et al. (1999) Hum Mol Genet 8, 763-74
– Lin et al. (2001) Hum Mol Genet 10, 137-44